Articles
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https://doi.org/10.55640/
METHODS OF BIOLOGICAL EXAMINATION OF THE ORIGIN OF AUTOIMMUNE LYMPHOPROLIFERATIVE SYNDROME AND ITS DETECTION
Kurbanova N.K. , Andijan State Medical Institute, UzbekistanAbstract
Autoimmune lymphoproliferative syndrome is a group of genetically determined diseases that occur due to hereditary or somatic mutations in the genes responsible for various stages of FAS-related apoptosis. Symptoms can be variable and most often include lymphadenopathy, splenomegaly, and various autoimmune lesions of the blood, liver, and thyroid systems. Diagnosis of autoimmune lymphoproliferative syndrome is based on the results of general and biochemical blood tests, lymph node biopsies, and genetic studies. There is currently no specific treatment for the disease, but a combination of immunosuppressive and cytotoxic therapy is used.
Keywords
Autoimmune lymphoproliferative syndrome , lymphadenopathy, splenomegaly.
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